Von Hippel-Lindau disease

on 19.1.09 with 0 comments

  • Characterized by cerebellar hemangioblastomas (benign tumors similar to plain hemangiomas, but they look like renal cell carcinoma, so they make it hard to tell if the tumor is a primary brain tumor or a metastasis), retinal angiomatosis, and visceral cysts

    • Visceral cysts are most common finding and can occur in the liver, pancreas, kidneys, etc

    • Also an increased risk of renal cell carcinoma in the kidneys

Category: Pathology Notes



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